Triple Localized Cranio-Facial Fibrous Dysplasia: A Case Report
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Keywords

fibrous dysplasia
polyostotic
craniofacial

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1.
Hamou M, Eabdenbitsen A, Elayoubi F, Ghailan MR. Triple Localized Cranio-Facial Fibrous Dysplasia: A Case Report. Integr J Med Sci [Internet]. 2019 Mar. 8 [cited 2024 Mar. 28];6. Available from: https://mbmj.org/index.php/ijms/article/view/103

Abstract

Introduction: fibrous dysplasia of bones is a non-hereditary congenital benign bone disorder, where normal bone is replaced by pseudofibrous tissue containing immature osteogenesis.
Case report: a 29-year-old patient with chronic hemodialysis who had a swollen mouth and hard palate that had been evolving for a year, impeding chewing and swallowing and causing facial asymmetry. Cranio-facial CT revealed multiple osteolytic bone-blast lesions, the histopathological study of which favored polyostotic fibrous dysplasia.
Discussion: fibrous dysplasia lesions may be single or multiple and may be responsible for pain and fragility, causing neurological complications in craniofacial localization. Imaging and, when a biopsy is needed, histology can establish the diagnosis. The treatment is based on bisphosphonates or, in special cases, surgical excision.

https://doi.org/10.15342/ijms.v6ir.257
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References

Couturier A, Aumaitre O, Mom T, Gilain L, André M. La dysplasie fibreuse osseuse cranio-faciale. Rev Med Interne. 2016 Dec; 37(12): 834-839. http://dx.doi.org/10.1016/j.revmed.2016.02.008

Couturier A, Aumaitre O, Gilain L, Jean B, Mom T, André M. Craniofacial fibrous dysplasia: A 10-case series. Eur Ann Otorhinolaryngol Head Neck dis. 2017 Sep; 134(4):229-235. http://dx.doi.org/10.1016/j.anorl.2017.02.004

Hanifi B, Samil KS, Yasar C, Cengiz C, Ecran A, Ramazan D. Craniofacial fibrous dysplasia, Clin Imaging. Nov-Dec 2013; 37(6): 1109-15. http://dx.doi.org/10.1016/j.clinimag.2013.01.010

Godse AS, Shrotriya SP, Vaid NS. Fibrous dysplasia of the maxilla. J Pediatr Surg. 2009 Apr ;44(4): 849-51. https://doi.org/10.1016/j.jpedsurg.2008.12.006

Chapurlat RD, Orcel P. Fibrous dysplasia of bone and McCune- Albright syndrome. Best Pract Res Clin Rheumatol. 2008 Mar; 22(1):55- 69. https://doi.org/10.1016/j.berh.2007.11.004

Turan S, Bastepe M. GNAS Spectrum of Disorders. Curr Osteoporos Rep. 2015 Jun; 13(3):146-58. https://doi.org/10.1007/s11914-015-0268-x

Akasbi N, Abourazzak FE, Talbi S, Tahiri L, Harzy T. La dysplasie fibreuse : état des lieux. Pan Afri Med J. 2015 May 8; 21(1): 21. https://doi.org/10.11604/pamj.2015.21.21.3487

Gensburger D, Chapurlat RD, Rey-Jouvin C, Orcel P. Prise en charge de la dysplasie fibreuse : recommandations actuelles et perspectives thérapeutiques. La Lettre du Rhumatologue. No 409- février 2015. [Accessed 03 Jul 2021]. Available From: https://www.edimark.fr/Front/frontpost/getfiles/22470.pdf

Numminen J, Rautiainen M. Polyostotic fibrous dysplasia of the mandible and bony nasal septum with intracranial expansion. Egyp J Ear Nose Throat Alli Sci. 2016 Mar; 17(1): 49-51. https://doi.org/10.1016/j.ejenta.2015.08.007

Béquignon E, Cardinne C, Lachiver X, Waqner I, Chabolle F, Baujat B. Craniofacial fibrous dysplasia surgery: A functional approach. Eur Ann Otorhinolaryngol Head Neck Dis. 2013 Sep; 130 (4):215-20. https://doi.org/10.1016/j.anorl.2012.07.005

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Copyright (c) 2019 Mahmoud Hamou et al.

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