Thoracic Manifestations of the Angiobehçet


atteinte cardiaque
localisation thoracique


How to Cite

Senhaji L, Alami B, Amara B, El Biaze M, Benjelloun MC, Serraj M. Thoracic Manifestations of the Angiobehçet. Integr J Med Sci [Internet]. 2019 Oct. 1 [cited 2024 Jun. 15];6. Available from:


Introduction: Vascular involvement in Behçet's disease affects 5 to 40% of patients. All vessels regardless of their type, size or location can be affected. This impairment is serious and can be life-threatening.
Patients and methods: We collected 12 cases from January 2010 to January 2017. These were 11 men and 1 woman with an average age of 32.5 years. The venous involvement involved 11 patients with thrombosis of the upper vena cava (VCS) in 6 patients, thrombophlebitis of the lower limbs in 5 patients, and thrombosis of the lower vena cava and hepatic veins in 1 patient. The arterial involvement affected 9 patients (75%) with an aneurysm of the pulmonary arteries in 5 patients and a pulmonary embolism in 5 others. The cardiac involvement concerned half of the patients with pericarditis type in 3 patients and intra-cardiac thrombus in 4 patients.
Conclusion: Thoracic involvement of the angiobehçet is frequent and severe, requiring rapid diagnosis and intense specific therapy to improve its prognosis.


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