Cor triatriatum sinister is a rare congenital cardiac anomaly in which a fibromuscular membrane divides the left atria into 2 chambers. It is even rarer when present at an adult age. Symptoms and presentation of the patient depend on the size of the opening into the membrane through which 2 chambers of the left atrium communicate with each other. Cor triatriatum sinister rarely remains asymptomatic till adulthood. In adults symptoms of Cor triatriatum sinister mimic the symptoms of mitral stenosis. Corrective surgery is the choice of treatment, but when it presents as an emergency case, especially at an early age, balloon dilatation of the membrane opening is done. Elective balloon dilatation of membrane opening at an early age diagnosed with Cor triatriatum sinister followed by corrective surgery at an adult age can be a safer option compared to direct corrective surgery at an early age. We present a case of a 25-year-old female who was diagnosed first time at this age as cor triatriatum sinister and treated successfully with corrective surgery.
Eichholz JL, Hodroge SS, Crook JJ 2nd, Mack JW Jr, Wortham DC. Cor Triatriatum Sinister in a 43-Year-Old Man with Syncope. Tex Heart Inst J. 2013;40(5):602-5.
Patel SV, Saggu A, Rajabalan A, Patel P, Singh T. Cor Triatriatum Sinister–A Rare Finding in Older Adult. Ann Cardiol Cardiovasc Med.2017; 1(1):1-3.
Van Praagh R, Corsini I. Cor triatriatum: Pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and as tudy of normal development of the pulmonary vein and atrial septumin 83 human embryos. Am Heart J. 1969 Sep;78(3):379-405. https://doi.org/10.1016/0002-8703(69)90046-5
Loeffler E. Unusual malformation of the left atrium: Pulmonary sinus. Arch Pathol (Chic). 1949 Nov;48(5):371–6.
van Son JA, Danielson GK, Schaff HV, Puga FJ, Seward JB, Hagler DJ, et al. Cor triatriatum: diagnosis, operative approach, and late results. Mayo Clin Proc. 1993 Sep;68(9):854-9. https://doi.org/10.1016/s0025-6196(12)60693-4
Narayanapillai J. Cor triatriatum sinister with severe obstruction: a rare presentation in an adult. BMJ Case Rep. 2016 Aug 5;2016:bcr2016215718. https://doi.org/10.1136/bcr-2016-215718
Khanra D, Soni S, Ola R, Duggal B. Cor triatriatum sinister presenting with acute myocardial infarction. J Pract Cardiovasc Sci. 2019;5(3):208-12. [Cited 2022 Mar 19]. Available from: https://www.j-pcs.org/article.asp?issn=23955414;year=2019;volume=5;issue=3;spage=208;epage=212;aulast=Khanra
Jayaprakash K, Madhavan S, Sudha Kumary V, George R, Cletus N, Baiju S. Wong’s anomaly –A rare variant of cor triatriatum. Indian Heart J. 2015 Sep-Oct; 67(5):469-71. https://doi.org/10.1016/j.ihj.2015.04.024
Jacopo S, Angelo B, Martina M, Paolo BG, Claudio B. Incidental Diagnosis of Non-Obstructive Cor Triatriatum Sinister. EC Cardiology. 2018; 5(10): 698-706. https://dx.doi.org/10.1186%2F1471-2261-10-54
This work is licensed under a Creative Commons Attribution 4.0 International License.
Copyright (c) 2020 Nagare K et al.